Search Results

31 - 40 of 59
Staff
Dr. Randy Chandler is an associate investigator in the Organic Acid Research Section of the Metabolic Medicine Branch in NHGRI.
… (MMA), propionic acidemia (PA), and Niemann-Pick Disease, Type C1. His preclinical proof-of-principal studies using MMA … to develop AAV gene therapy to treat Niemann-Pick Disease, Type C1 disease, a rare and lethal inherited neurological … therapy with a neurotrophic capsid in Niemann-Pick disease type C1 mice . Life Sci Alliance . 2021. May FJ, Head PE, …
Staff
Dr. Wilson is the co-chief of and senior investigator in NHGRI's Computational and Statistical Genomics Branch.
… identify statistical challenges that need to be addressed, 2) to develop new methods of genetic analysis for … are statistically valid and have reasonable power and type I error rates. Software packages developed include 1) … was discovered that there was a substantial inflation of type I error when GWAS methods were used to analyze rare …
Staff
Dr. Amanda Ombrello is a clinical researcher in the Inflammatory Disease Section of NHGRI's Medical Genetics Branch.
… devastating disease, deficiency of adenosine deaminase 2.  She has also worked in conjuncture with the CD22 CAR-T … AK . The spectrum of the deficiency of adenosine deaminase 2: An observational analysis of a 60 patient cohort . Front … MA, Aksentijevich I, Kastner DL, Milner JD, Ombrello AK . Type I interferon signature predicts response to JAK …
Staff
Dr. Tyra Wolfsberg is the associate director of the Bioinformatics and Scientific Programming Core at the National Human Genome Research Institute. ​
… ctenophore Mnemiopsis leidyi and its implications for cell type evolution. Science , 342(6164):1242592. 2013. [ PubMed ] … hematopoietic stem and progenitor cells. PLoS Biology, 2:2183-2190. 2004. [ PubMed ] Instructional Videos Current …
Staff
Dr. Peter McGuire is an investigator in NHGRI's Center for Precision Health Research.
… activation on end-organ mitochondrial metabolism; and 2) the role of mitochondria in immune cell function. Immune … combined methylmalonic aciduria and homocystinuria, cblC type, and utility of methionine as a secondary screening … transfer rescues a lethal murine model of citrullinemia type 1. Gene Ther, 20:1188-1191 . 2013. [ PubMed ] McGuire, …
Staff
Dr. Pamela Schwartzberg is a adjunct investigator in NHGRI's Genetic Disease Research Branch.
… DB, Schwartzberg PL.  The TCF1-Bcl6 axis counteracts type I interferon to repress exhaustion and maintain T cell … of post-vaccination responses .  Cell . 2014 Apr 10;157(2):499-513. *co-corresponding authors Gomez-Rodriguez J, …
Staff
Dr. Carsten Bonnemann is an adjunct investigator in the Medical Genetics Branch at the National Human Genome Research Institute. ​
… Sciot, C.G. Bönnemann. Predominant fiber atrophy and fiber type disproportion in early Ullrich disease. Muscle & Nerve , … Darras, L.M. Kunkel. A mutation in the alpha 3 chain of type IX collagen causes autosomal dominant multiple …
Staff
Dr. David Bodine is the chief of and senior investigator in NHGRI's Genetics and Molecular Biology Branch.
… lineages and eventually become committed to one single type of cell that ultimately enters the blood circulation. … stem cells contain high levels of mRNA for c-kit, GATA-2, p45NF-E2 and c-myb, and low levels or no mRNA for c-fms …
Staff
Dr. Stone is a staff clinician in NHGRI's Inflammatory Disease Section.
… where she then continued as a Senior Staff Fellow for 2 years. In 2007, she joined Dr. Daniel Kastner’s group that … subunit mutations in CANDLE/PRAAS patients promote type I IFN production . J Clin Invest . 2015 Nov … E.  Glucocerebrosidase gene mutations in patients with type 2 Gaucher disease .  Hum Mutat . 2000: 15(2):181-8. …
Staff
Dr. Laura Elnitski is a senior investigator in the Translational and Functional Genomics Branch at the National Human Genome Research Institute. ​
… hyperactivity disorder . Mol Psychiatry . 2023 Feb;28(2):792-800. doi: 10.1038/s41380-022-01844-9. Epub 2022 Nov …